Considerations for Fontan Individualization in Patients with Isomerism (Heterotaxy)
نویسندگان
چکیده
Fontan palliation has been used as the final stage in functionally univentricular palpation for several years. The Fontan has undergone several iterations, having begun as an atriopulmonary connection and then evolving into the extracardiac conduit. Innovations in computer modeling and flow simulation has now allowed for studies to be conducted to characterize flow within the Fontan conduit and compare the efficiency of various different Fontan geometries. We review data pertaining to various Fontan geometries in this manuscript”.
منابع مشابه
Improving results of the Fontan procedure in patients with heterotaxy syndrome.
BACKGROUND The Fontan operation in patients with heterotaxy syndrome has been associated with a poor prognosis. We studied whether the outcome of those patients with heterotaxy syndrome improved compared with those who did not have the syndrome after an extracardiac Fontan operation. METHODS A retrospective review was performed on 185 patients who had undergone an extracardiac Fontan operatio...
متن کاملHeterotaxy Syndrome
Heterotaxy is defined as an abnormality where the internal thoraco-abdominal organs demonstrate abnormal arrangement across the left-right axis of the body. This broad term includes patients with a wide variety of very complex cardiac lesions. Patients with heterotaxy can be stratified into the subsets of asplenia syndrome and polysplenia syndrome, or the subsets of heterotaxy with isomerism of...
متن کاملEarly and late results of the modified fontan operation for heterotaxy syndrome 30 years of experience in 142 patients.
OBJECTIVES We sought to evaluate the early and late results of the modified Fontan operation for patients with heterotaxy syndrome, assess variables traditionally known to correlate with poor outcome, and assess current health status of survivors after the Fontan procedure. BACKGROUND The natural history of unoperated cardiac lesions in heterotaxy is known to be poor. Therefore, the Fontan op...
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So-called "heterotaxy" is a laterality defect characterized by isomerism of the thoracic organs and random arrangement of the abdominal organs. These findings go beyond anatomic curiosity and have functional implications. It is, thus, of the utmost importance to be able to properly identify these findings. Radiologic studies can be invaluable in determining anomalies in the central nervous, pul...
متن کاملFontan Operation in a Patient with Severe Hypoplastic Right Pulmonary Artery, Single Ventricle, and Heterotaxy Syndrome.
Assessment of the pulmonary circulation status including pressure, resistance, size, and absence of anatomical distortion, is crucial to the successful Fontan operation. Most patients are found to have acceptable pulmonary arteries after previous palliation, although some degree of distortion is not uncommon. However, in rare instances, some patients have only one functioning lung with another ...
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